特发性肺间质性肺炎(IIP),是以弥漫性肺泡炎和肺泡结构紊乱最终导致肺纤维化为特征的进行性下呼吸道疾病,发病原因未明。一、关于命名:1935年Hamman和Rich在美国报道了4例严重的呼吸困难、紫绀患者,均在半年内死亡。之后,本病命名为Hamman-Rich氏综合征。之后,学者们发现多数患者病情较为缓慢,遂提出不同命名。欧洲通常称为隐原性致纤维化肺泡炎(Cryptogenic fibrosing alveolitis CFA),日本称为 Idiopathic pulmonary interstitial pneumonia (IIP) is a progressive lower respiratory disease characterized by diffuse alveolitis and disorganization of the alveoli, which eventually leads to pulmonary fibrosis. The cause of the disease is unknown. First, on the naming: Hamman and Rich in 1935 reported four cases of severe dyspnea in the United States, cyanosis patients were killed within six months. After the disease is named Hamman-Rich’s syndrome. Later, scholars found that the majority of patients were more slowly, then made a different name. Commonly known as Europe Cryptogenic fibrosing alveolitis (Cryptogenic fibrosing alveolitis CFA), Japan called