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1 患者,男性,8岁,学生.出生后即有左前左前臂旋转障碍,因作残疾鉴定需要来我院检查.患儿孕1产1、足月顺产,无外伤史,无家族史.2 体检 左前臂旋转功能障碍、固定于旋前位,肘关节伸屈功能正常,双侧前臀长短无明显差异,其它四肢无畸形.X线:左尺桡骨近端骨性融合,骨小梁串通,骨皮质相连,连接处宽约30mm,尺骨鹰嘴发育正常,桡骨发育尚好,近端向后脱位.诊断:尺桡骨近端先天性骨连接.3 小儿尺桡骨先天性骨连接极为少见.病因:桡尺骨起源于同一中胚层组织所衍化出来的软骨枝,当软骨枝纵向分节发育过程终止或两骨近端的间隙中充满中胚层组织并发生骨化均可引起此畸形.Wilkie认为:此种畸形有两种类型:Ⅰ型:尺桡骨髓腔相连,桡骨近端变形并与尺骨连接,桡骨比尺骨长而粗大.Ⅱ型:桡骨基本正常,它的近端
1 patient, male, 8 years old, students.After birth, left front left forearm rotation disorder, due to disability identification need to come to our hospital for examination .Pregnant 1 birth 1, full-term follow-up, no history of trauma, no family history.2 Physical examination left forearm rotation dysfunction, fixed in anterior pronation, elbow flexion and extension of normal function, bilateral anteromedial length no difference, no other limbs deformity.X line: the left ulna radial bone proximal fusion, trabecular collation , Cortical bone connected to the junction width of 30mm, olecranon normal development, radial development is still good, proximal posterior dislocation. Diagnosis: proximal radius and ulna bone congenital bone .3 pediatric radius and ulna congenital bone link is extremely rare. : Radial ulnar originated from the same mesoderm derived from the cartilage branch, when the longitudinal division of the cartilage branch of the end of the development process or the gap between the proximal two bones full of mesodermal tissue and ossification can cause this deformity.Wilkie that: There are two types of deformities: type I: ulna and medullary canal connected to the proximal radial deformation and connected with the ulna, the radius is longer and thicker than the ulna.II type: the radius is normal, its proximal