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目的探讨儿童支气管类癌的临床病理学特征及病理诊断。方法结合我院2例临床资料及组织学观察和免疫组化研究复习有关文献进行分析讨论。结果2例均为中央型支气管类癌,瘤细胞排列成实性片状、小梁状及乳头状;细胞大小一致,胞浆嗜酸性,胞核圆形,核分裂罕见。免疫组化标记CK、Syn、CgA及NSE均阳性。结论儿童支气管典型类癌为高分化神经内分泌癌。由于支气管肿瘤在儿童较罕见,临床症状缺乏特异性,极易引起临床误诊,延误治疗,须引起高度重视。
Objective To investigate the clinicopathological characteristics and pathological diagnosis of children with bronchial carcinoid. Methods Two cases of our hospital clinical data and histological observation and immunohistochemical study review the literature for analysis and discussion. Results The two cases were all central bronchial carcinomas. The tumor cells were arranged in the form of solid flake, trabecular and papillary. The cells were of the same size and cytoplasm had eosinophilicity, round nucleus and rare mitosis. Immunohistochemical markers CK, Syn, CgA and NSE were positive. Conclusion The typical bronchial carcinoid in children is highly differentiated neuroendocrine carcinoma. Because bronchial tumors are rare in children, the lack of specificity of clinical symptoms, can easily lead to clinical misdiagnosis, delay treatment, must pay close attention.