先天性巨输尿管症系输尿管发育畸形 ,为少见疾病。笔者遇到 1例 ,报告如下。女 ,47岁。自诉入院前二天突感右下腹阵发性疼痛伴双侧腰痛 ,在当地卫生院对症治疗不见好转 ,即前来我院。外科查体 :右下腹压痛 ,反跳痛 (± ) ,腹肌平软 ,肠鸣音正常 ,右肾区叩击痛阳性。辅助检查 :? Congenital giant ureteric ureteric deformity, a rare disease. I met one case, the report is as follows. Female, 47 years old. Self-prosecution two days prior to admission suddenly felt right lower quadrant paroxysmal pain with bilateral low back pain, symptomatic treatment at the local hospital did not improve, that is, to come to our hospital. Surgical examination: right lower quadrant tenderness, rebound tenderness (±), abdominal muscle soft, normal bowel sounds, right renal percussion pain positive. Auxiliary examination:?