原发性干燥综合征(primary Sj9gren’s syndrome,p SS)是一种原发性的,不与其它结缔组织病并存的,以侵犯外分泌腺为主,并可累及多器官、多系统的慢性炎症性自身免疫疾病。p SS可影响中枢和周围神经系统,周围神经系统更易受累。与以往文献报道的pSS合并周围神经病多数累及感觉神经不同,本病例的特点是仅表现为四肢无力、单侧面瘫的运动神经损伤症状,不累及感觉神经,临床较少见。 Primary Sjgren’s syndrome (pSs) is a primary disease that does not coexist with other connective tissue diseases and mainly affects the exocrine glands and can affect multiple organs and multiple systems of chronic inflammation Autoimmune diseases. p SS can affect the central and peripheral nervous system, the peripheral nervous system more susceptible. Unlike previous reports of pSS complicated peripheral neuropathy involving the sensory nerve, this case is characterized by only manifested as limb weakness, unilateral paralysis of motor nerve injury symptoms, does not affect the sensory nerve, clinical less common.