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免疫球蛋白缺乏综合征(或称低丙种球蛋白血症)涉及肠道者称为免疫球蛋白缺乏综合征肠病。近年来随着免疫学的发展和临床经验的累积,对这种病的认识有所提高。现就其小肠 X 线表现有关问题综述如下。一、免疫球蛋白缺乏综合征的免疫学基础机体的免疫防御机制可分为两类,一为细胞介导免疫,另一为体液介导免疫即免疫球蛋白免疫,两者均与淋巴细胞有关。淋巴细胞的干细胞分化成胸腺前细胞,在胸腺激素的影响下变为 T-淋巴细胞,负责细胞免疫机制.淋巴干细胞分化而成的 B-淋巴细胞,在特殊抗原的作用下变成浆细胞。不同的浆细胞产生不同的免疫球蛋白,负责体液免疫机制.淋巴干细胞变成 B-淋巴细胞,在人体是由相当于鸡胚Fabricius 囊的淋巴样器官的淋巴组织所控制的,
Immunoglobulin deficiency syndrome (or hypoalbuminemia) involving the gut is called immunoglobulin deficiency syndrome enteropathy. In recent years, with the development of immunology and the accumulation of clinical experience, awareness of this disease has increased. Now on the performance of small bowel X-ray related issues are summarized below. First, immunoglobulin deficiency syndrome based on the basis of immunology Immune defense mechanism of the body can be divided into two categories, one for cell-mediated immunity, and the other for the humoral-mediated immunity that immunoglobulin immunization, both with lymphocytes . Lymphocyte stem cells differentiate into thymocytes, which become T-lymphocytes under the influence of thymus hormones and are responsible for cellular immune mechanisms. B-lymphocytes, which are differentiated from lymphoid stem cells, become plasma cells under the action of specific antigens. Different plasma cells produce different immunoglobulins and are responsible for the humoral immune mechanism.The lymphoid stem cells become B-lymphocytes, which are controlled in the human body by lymphoid tissues corresponding to the lymphoid organs of the chicken embryo Fabricius sac,