系统性红斑狼疮(Systemic Lupus Erythematosus,SLE)是一种累及全身各器官系统的自身免疫性疾病,心脏是常见的受累器官之一。临床多见的是心包炎、心内膜炎、心肌炎及冠状动脉病,并发肺 动脉高压(Pulmonary Arterial Hypertension,PAH)比较少见。本文对我院1992年以来收治的资料较全面的163例SLE进行了回顾性分析,发现其中5例伴有PAH征。现报告如下。 1 临床资料 例1,女,41岁。因脱发、反复口腔溃疡、关节痛,伴发热三年,心悸、渐进性呼吸困难、双下肢浮肿 Systemic Lupus Erythematosus (SLE) is an autoimmune disease that affects various organs and systems of the body. The heart is one of the common organs involved. More common in clinical pericarditis, endocarditis, myocarditis and coronary artery disease, pulmonary hypertension (Pulmonary Arterial Hypertension, PAH) is relatively rare. This article retrospectively analyzed 163 cases of SLE admitted to our hospital since 1992 and found that 5 cases were accompanied by PAH sign. The report is as follows. 1 clinical data example 1, female, 41 years old. Due to hair loss, repeated oral ulcers, joint pain, fever with three years, palpitations, progressive dyspnea, lower extremity edema