先天性肺发育不全是一种少见的先天性肺、支气管发育畸形,发病率为1.4‰,占早期新生儿死亡的15%~20%。为提高认识,做到早发现、早治疗,报告2例该病诊疗并文献复习如下。例1:患儿,女,60d,由于“生后即呼吸急促,加重伴喘鸣音2天”入院。患儿系足月顺产,生后发现呼吸略急促,剧烈哭闹时口周发青,社区医师曾经2次探访,未予结论。入院前2天,因呼吸急促加重,伴有喘鸣,烦躁不安,以“支气管肺炎”收住院。入院 Congenital lung hypoplasia is a rare congenital lung, bronchial malformations, the incidence was 1.4 ‰, accounting for early neonatal mortality of 15% to 20%. To enhance awareness, early detection, early treatment, report of 2 cases of the disease diagnosis and treatment of the literature review as follows. Example 1: Children, female, 60d, due to “shortness of breath after birth, increased with wheezing 2 days ” admission. Children with full-term follow-up of abortion, after birth, found that breathing slightly faster, severe blues when mouth week blue, community physicians had two visits, no conclusion. 2 days before admission, due to shortness of breath increased, accompanied by wheezing, irritability, to “bronchial pneumonia,” admitted to hospital. Admission