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目的:探讨颈部节细胞神经瘤的临床特点、诊断、治疗方式及预后。方法:回顾性分析1995-2009年收治的6例颈部节细胞神经瘤患者的临床资料并进行总结。结果:患者临床多表现为颈部无症状肿物,术前影像学检查及细针穿刺细胞学检查未能明确诊断。患者均接受手术治疗,术后均出现Horner征。术后随访1~17年,中位随访时间5.9年。患者均生存,肿瘤无复发或转移。结论:颈部节细胞神经瘤是一种罕见的分化较好的良性肿瘤,一般需行病理学检查才能明确诊断。手术是惟一治疗手段,完整切除肿瘤后患者预后良好。
Objective: To investigate the clinical features, diagnosis, treatment and prognosis of cervical ganglioneuroma. Methods: The clinical data of 6 patients with cervical ganglioneuromas treated in our hospital from 1995 to 2009 were retrospectively analyzed and summarized. Results: The clinical manifestations of asymptomatic neck patients, preoperative imaging and fine needle aspiration cytology failed to confirm the diagnosis. All patients underwent surgery, Horner sign appeared after surgery. The patients were followed up for 1 to 17 years and the median follow-up time was 5.9 years. All patients survived without tumor recurrence or metastasis. Conclusion: Cervical ganglioneuroma is a rare well-differentiated benign tumor, usually need pathological examination to confirm the diagnosis. Surgery is the only treatment, patients with complete resection of the tumor prognosis is good.