先天性耳畸形可合并面神经畸形,较少见,兹报道如下: 患者男,17岁,因左耳畸形伴听力障碍17年入院。患者自出生时即发现左耳外观异常,但未诊治,随年龄增长,左右差异日渐明显,听力受影响,其余无不适。家族中无同类病史,其母孕期曾患感冒。全身检查未见异常。专科检查左耳廓仅耳垂存留,外耳道口水平以下结构缺失,耳垂向前倾倒,外耳道呈浅漏斗状,其余均闭锁。右耳正常。音叉检查左耳传导性重听。电测听检查左耳气 Congenital malformations of the antrum can be associated with facial nerve deformities, less common, it is reported as follows: Male patient, 17 years old, left ear deformity with hearing impairment 17 years admitted. Patients found that the appearance of the left ear abnormalities at birth, but not diagnosed and treated, with age, the difference between the obvious obvious, hearing affected, the rest without discomfort. No similar family history, her mother had had a cold during pregnancy. No abnormalities in the whole body examination. Only a left ear examination specialist left ear retention, the level of the external auditory meatus below the level of structure loss, earlobe forward dumping, external auditory canal funnel-shaped, the rest are blocked. Right ear normal. Tuning fork check left ear conductive re-listen. Electric audiometry check left ear gas