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目的:探讨肾上腺嗜铬细胞瘤自发破裂的临床病例特征,提高对肾上腺嗜铬细胞瘤自发破裂的认识。方法:对1例肾上腺嗜铬细胞瘤自发破裂出血急诊患者的临床诊治及影像学特点结合相关文献进行分析。结果:以急腹症发病,表现为剧烈的腰、腹部疼痛伴高血压,同时有失血性休克表现;B超、CT检查提示肾上腺区肿瘤并破裂、肾周血肿。结论:肾上腺嗜铬细胞瘤可能会发生自发破裂而出血,B超、CT检查有助于诊断,治疗常需手术切除肿瘤、清除血肿。
Objective: To investigate the clinical features of spontaneous rupture of adrenal pheochromocytoma and to improve the understanding of spontaneous rupture of adrenal pheochromocytoma. Methods: The clinical diagnosis, treatment and imaging features of a patient with spontaneous rupture of adrenal pheochromocytoma were analyzed. Results: The incidence of acute abdomen, manifested as severe waist, abdominal pain with hypertension, and hemorrhagic shock at the same time; B-ultrasound, CT examination showed adrenal gland tumor and ruptured, perirenal hematoma. CONCLUSIONS: Adrenal pheochromocytoma may undergo spontaneous rupture and hemorrhage. B-ultrasonography and CT examination are helpful in the diagnosis. The treatment often requires surgical resection and hematoma removal.