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胃肠道间质瘤(gastrointestinal stromal tumour,GIST)过去常与平滑肌瘤和平滑肌肉瘤相混淆。现在GIST被定义为一种免疫表型上表达kit蛋白(CD117)和CD34、遗传上存在频发性c-kit基因突变、组织学上以富于梭形细胞、上皮样细胞或多形性细胞的呈束状或弥散性排列为特征的胃肠道间叶源性
Gastrointestinal stromal tumor (GIST) used to be confused with leiomyoma and leiomyosarcoma. Now that GIST is defined as an immunophenotypically expressed kit protein (CD117) and CD34, there are genetically frequent mutations in the c-kit gene that are histologically characterized by abundant spindle-shaped cells, epithelioid or pleomorphic cells In a bundle or diffuse arrangement characterized by gastrointestinal mesenchymal origin