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先天性红细胞生成障碍性贫血(CongenitalDyserythropoitic Anemia)简称CDA。是一种少见的遗传性贫血,主要特点是骨髓红细胞系统核的分裂和成熟障碍,红细胞无效造血,表现为难治性贫血。CDA成为独立的一类疾病是Crookston等(1966)
Congenital Dysplastic Anemia CongenitalDyserythropoiticAnemia referred to as CDA. Is a rare hereditary anemia, the main feature is the division of bone marrow erythroid system and maturation of obstacles, hematopoietic failure of red blood cells, showing refractory anemia. A category of CDA that becomes independent is Crookston et al. (1966)