骨神经外胚层肿瘤较为罕见,现将我们所遇1例报道如下。患者,男性,17岁,因右上臂疼痛逐渐加重并出现局部肿胀2个月入院。体检结果:一般状况中等,贫血貌,全身皮肤及黏膜无黄染、出血、水肿,浅表淋巴结未触及肿大,心肺腹无阳性体征。右肩部可见片状色素沉着区,右上臂中段内侧明显 Bone nerve ectodermal tumors are relatively rare, now we encounter a case reported as follows. The patient, male, 17 years old, was gradually hospitalized with pain in his right upper arm and had a local swelling for 2 months. Physical examination results: general condition, anemia, systemic skin and mucous membrane without yellow dye, bleeding, edema, superficial lymph nodes did not touch swollen, no positive signs of cardiopulmonary abdominal. The right shoulder visible patchy pigmentation area, medial right upper arm obvious