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神經纤维瘤病,为一較少見之疾病。国內1955年上海医学院报告2例(1例在1941年)中枢型神經紆維瘤病,1958年罗德元报告一例多发性神經(膜)纤維瘤病伴发多发性脑膜瘤。本院曾迴到一例多发性神經纤維瘤病,經病理检查証实,报告如下: 患者宋×香,女性,17岁,农,未婚,山东汶上人。入院日期:1961年12月11日。住院号4987,X光号21845,病理号(济宁医专)1339/61。主訴:右側头面部肿胀已三年。在十年前即发現右耳后和腰背部生长一些大如黄豆,小如綠豆之肿物数个,不疼不痒,沒有紅肿,除触之肿物有些发麻外,其他没有任何感觉,近三年来右耳后肿物逐漸长大,且向四周漫延伸展,右耳肥厚变大下垂,听力沒有影响,无头疼、头暈、恶心、呕吐等症状,至今无月經来潮。近几年來患者記忆力和智力逐漸減退,精神迟鈍。
Neurofibromatosis, a rare disease. In 1955, Shanghai Medical College reported 2 cases (1 case in 1941) of central neurovascular disease. In 1958, Rhode yuan reported a case of multiple neurofilament diseases with multiple meningioma. Our hospital has returned to a case of multiple neurofibromatosis, confirmed by pathological examination, the report is as follows: Patient Song × Hong, female, 17 years old, farming, unmarried, Wenshang Shandong. Date of admission: December 11, 1961. Hospital No. 4987, X-ray 21845, pathology (Jining Medical) 1339/61. Chief complaint: swelling of the right head and face has been three years. Ten years ago found that the growth of the right ear and back and some as large as soybeans, small beans, such as the number of mung bean few, itching does not itch, no redness, in addition to touch the tumor some numb, the other without any Feeling, the past three years, the right ear, the tumor gradually grew up, and extended to the surrounding extended, right ear hypertrophy drooping, hearing had no effect, no headache, dizziness, nausea, vomiting and other symptoms, so far no menstrual cramps. In recent years, memory and intelligence gradually decline, mental retardation.