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本文报道与明确自身免疫疾病有关的不明原因的骨髓样化生(AMM)1例,并讨论两者的关系。女性,24岁。因进行性四肢乏力入院,体查除神经系统发现上肢腱反射减弱和下肢腱反射消失外,其余正常,血常规和生化正常,脑脊液除蛋白340mg%外,未发现细胞。患者既有抗体又有对外周神经蛋白P_1L及纯化乙酰胆碱受体细胞介导的免疫迹象,有冷球蛋白血症和荧光抗核抗体试验阳性,狼疮细胞和抗DNA抗体阴性。连续肌电描记研究符合神经病变,张力试
This article reports one case of unexplained myeloid metaplasia (AMM) associated with a definite autoimmune disease and discusses the relationship between the two. Female, 24 years old. Due to progressive limb weakness admitted to the hospital, physical examination in addition to the nervous system found upper limb tendon reflexes and lower extremity tendon reflex disappeared, the rest of the normal blood and biochemical normal cerebrospinal fluid in addition to protein 340mg%, no cells were found. Patients had both antibodies and peripheral nerve protein P_1L and purified acetylcholine receptor cell-mediated immune signs, cryoglobulinemia and fluorescent anti-nuclear antibody test positive, lupus cells and anti-DNA antibody negative. Continuous electromyography consistent with neuropathy, tension test