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作者收集匹兹堡儿童医院1968～1976年间所诊断为环咽肌失弛症的儿童15例。12例在出生时即有症状,另3例分别在出生后一个月、四个月和六个月时出现进食不便、咽部充血、进食时窒息、呛咳、反胃和鼻腔反流等症状。虽然12例于出生后就有症状,但亦并非当时就能明确诊断。 5例作食管蠕动研究,均显示环咽肌失弛,3例见环咽肌不能松弛。1例开始时压力升高,继之有一轻微松弛现象,随后即出现痉挛。1例食管括约肌持续痉挛达10秒。这5例的食管其它部位还有异常蠕动,如下食管括约肌松弛失灵,在上、下括约肌间可见双相波、逆行波和跳跃区。2例无伴发症和无症状的病例随访七年,其
The authors collected 15 cases of children diagnosed with Cricopharyngeal muscular dystrophy from 1968 to 1976 at Pittsburgh Children’s Hospital. Twelve cases were symptomatic at birth and the other three had symptoms of inconvenience of eating, pharyngeal congestion, asphyxiation, choking, nausea and nasal reflux during one, four and six months of life, respectively. Although 12 patients had symptoms after birth, it was not clear at the time that they were diagnosed. 5 cases of esophageal peristalsis study, showed cricopharyngeal muscle discomfort, 3 cases of cricopharyngeal muscle can not be relaxed. One patient started with a pressure increase followed by a slight relaxation followed by convulsions. One case of esophageal sphincter sustained spasm for 10 seconds. The other 5 cases of esophageal abnormal motility, such as the following esophageal sphincter relaxation failure, in the upper and lower sphincter visible biphasic waves, retrograde waves and jumping area. Two cases of non-complication and asymptomatic cases were followed up for seven years