特发性肺含铁血黄素沉着症(Idiopathic pulmo-nary Hemosiderosis,下简称IPH)最早先由Virchow(1864)报告其病理学特征,67年后Ceelan(1931)在尸检中发现了两例并总结了本病的临床特征,之后相继有病例报告。国内1960年首由吴氏报告1例后,迄今共报告146例(包括本文9例),这些病例报告主要来自我国北方(北京、甘肃、四川等地),南方的报道甚少。本症系一少见病,多数发生于小儿时期,临床方面认识不足,常易造成误诊、漏诊,因此仍有加深认识的必要。现将我们诊断的9例予以报告,并拟结合文献复习,进行分析讨论。 Idiopathic pulmo-nary hemosiderosis (IPH) was first reported by Virchow (1864) for its pathological features and 67 years later, Ceelan (1931) found two cases in autopsy and concluded The clinical features of the disease, followed by case reports. A total of 146 cases (including 9 cases) have been reported in China since the first report by Wu in 1960 in China. The reports of these cases mainly come from the northern part of China (Beijing, Gansu and Sichuan). The disease is a rare disease, most of which occurred in infancy, lack of understanding of clinical aspects, often misdiagnosis, missed diagnosis, there is still a need to deepen understanding. Now we diagnosed in 9 cases to be reported, and the literature to be reviewed, analysis and discussion.