多发性肌炎(PM)/皮肌炎(DM)为侵犯横纹肌的炎性肌病,多发于颈咽肌、四肢近端肌及腰肌,严重时呼吸肌亦有损害,病情发展迅速,危及生命。一般治疗应用皮质类固醇激素类及免疫抑制剂,也有应用血浆置换治疗收到良好效果,但采 Polymyositis (PM) / dermatomyositis (DM) is an inflammatory myopathy that affects striated muscle, which occurs in the neck and throat muscles, proximal limb muscles and psoas. Severe respiratory muscles are also damaged. The disease develops rapidly and is at risk life. The general treatment of corticosteroids and immunosuppressive agents, but also the application of plasma exchange treatment received good results, but mining