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胰腺实性-假乳头状瘤(solid-pseudopapillary tumors of pancreas,SPT)是一种较少见的、好发于青年女性的胰腺肿瘤,1959年由Frantz[1]首先报道,该肿瘤又称为实性囊性或乳头状囊性肿瘤、实性和乳头状上皮性肿瘤和Frantz瘤等,2004年世界卫生组织(WHO)肿瘤病理学分类中将其列为胰腺外分泌源性肿瘤,统一命名为胰腺实性-假乳头状瘤,由形态比较一致的细胞形成实性巢状和乳头状结构的上皮性肿瘤,常有出血、坏死及囊性变,常表现为良性过程,偶尔可为恶性,本研究收集了5例经过病理明确诊断的SPT,并结合文献探讨其临床表现、免疫病理学特征、诊断及鉴别诊断,以提高对SPT的认识。
Pancreatic solid pseudopapillary tumors of the pancreas (SPT) is a rare pancreatic tumor that occurs in young women. It was first reported by Frantz [1] in 1959 that the tumor was also called Solid cystic or papillary cystic tumors, solid and papillary epithelial tumors and Frantz tumors, 2004 World Health Organization (WHO) classification of tumor pathology as pancreatic exocrine tumors, unified named Pancreatic solid-pseudopapillary tumor, the formation of solid nests and papillary structures of epithelial tumors from relatively consistent cells, often with bleeding, necrosis and cystic degeneration, often manifested as a benign process, and occasionally can be malignant, This study collected 5 cases of pathologically diagnosed SPT, combined with the literature to explore its clinical manifestations, immunopathological features, diagnosis and differential diagnosis to improve awareness of SPT.