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目的:探讨头颈部炎性肌纤维母细胞瘤的临床病理特点、治疗方法及疗效。方法:回顾性分析6例经病理确诊的头颈部炎性肌纤维母细胞瘤患者的临床资料。结果:6例患者均行手术治疗,随访6个月~7年。至末次随访,2例死亡,2例带瘤生存,2例无瘤生存。结论:炎性肌纤维母细胞瘤最多发生于肺,发生于头颈部者极为罕见。诊断主要依靠病理及免疫组织化学检测。治疗以手术扩大切除为主,术后复发率较高,需长期随访。术后放化疗疗效差。
Objective: To investigate the clinicopathological features, treatment methods and curative effects of inflammatory myofibroblastic tumors in the head and neck. Methods: The clinical data of 6 patients with pathologically diagnosed inflammatory myofibroblastic tumors of the head and neck were retrospectively analyzed. RESULTS: Six patients underwent surgical treatment and were followed up for 6 months to 7 years. To the final follow-up, 2 patients died, 2 patients survived with tumor, and 2 patients survived without tumor. Conclusion: Inflammatory myofibroblastic tumors occur most frequently in the lungs and are extremely rare in head and neck areas. Diagnosis depends mainly on pathological and immunohistochemical detection. The treatment is mainly surgical resection and recurrence rate is high, requiring long-term follow-up. Postoperative radiotherapy and chemotherapy were poor.