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肺动脉高压(pul monary arterial hypertension,PAH)是一种以循环中CD34+CD133+促血管生成的祖细胞和病理性表达缺氧诱导因子1(hypoxia-induc-ible factor1,HIF-1)的内皮细胞数量增多为特征的增生性血管病变。与健康对照组相比,PAH患者的骨髓、血液和肺动脉中的CD34+CD133+祖细胞数量较多。在PAH患者的血液中,HIF诱导的骨
Pulmonary arterial hypertension (PAH) is a type of endothelial cell that circulates CD34 + CD133 + proangiogenic progenitor cells and pathologically-expressed hypoxia-induc-ible factor 1 (HIF-1) Increased features of proliferative vascular disease. PAH patients had more CD34 + CD133 + progenitor cells in the bone marrow, blood and pulmonary arteries than healthy controls. HIF-induced bone in PAH patient’s blood