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小儿ChiariⅠ型畸形合并脊髓空洞症临床少见,患儿临床症状较少、隐袭且与成年人有很大区别,容易发生误诊、误治。随着MRI的广泛应用,该疾病诊断数量日渐增多,但目前关于小儿ChiariⅠ型畸形合并脊髓空洞症的研究存在较多争议,临床工作者对其认识和诊治水平尚待提高。根据国内外文献、专著及最新临床试验研究成果,现就小儿ChiariⅠ型畸形合并脊髓空洞症研究进展进行综述。
Pediatric Chiari type I deformity associated with syringomyelia is rare, clinical symptoms in children less insidious and adults are very different, prone to misdiagnosis, mistreatment. With the wide application of MRI, the number of diagnosis of this disease is increasing day by day. However, there is much controversy about the study of Chiari Ⅰ malformation associated with syringomyelia in children. The level of understanding and diagnosis of Chiari Ⅰ remains to be improved. According to the domestic and foreign literature, monographs and the latest clinical trial research results, the research progress of children with Chiari Ⅰ deformity combined with syringomyelia are reviewed.