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皮肌炎的临床表现多种多样,易误诊误治。作者通过对17例患儿病例分析,讨论其误诊原因。其中男7例,女10例。年龄~1岁1例,~5岁4例,~10岁8例,~14岁4例。入院前病程~3个月5例,~6个月5例,~12个月3例,1年以上4例。首发症状不一,有乏力、全身不适15例,发热7例,眼睑浮肿9例,眼睑及鼻梁紫红色斑9例,面部皮疹7例,头面毛发过多4例,面部毛细血管扩张3例,全身红斑皮疹5例,行走困难7例等。实验室检查:轻度贫血12例,中度3例;周围血白细胞计数高于10×10~9/L15例,最高31
Dermatomyositis a variety of clinical manifestations, easy misdiagnosis and mistreatment. The authors analyzed 17 cases of children to discuss the causes of misdiagnosis. There were 7 males and 10 females. 1 patient aged ~ 1 year, 4 patients ~ 5 years old, 8 patients ~ 10 years old and 4 patients ~ 14 years old. Pre-admission course ~ 3 months in 5 cases, ~ 6 months in 5 cases, ~ 12 months in 3 cases, more than 1 year in 4 cases. The first symptom was varied, with weakness, 15 cases of general malaise, 7 cases of fever, 9 cases of eyelid edema, 9 cases of eyelid and nasal purple spots, 7 cases of facial rash, 4 cases of excessive facial hair, 3 cases of facial telangiectasias, 5 cases of systemic erythema rash, walking difficulties in 7 cases. Laboratory tests: mild anemia in 12 cases, moderate in 3 cases; peripheral blood leukocyte count higher than 10 × 10 ~ 9 / L in 15 cases, the highest 31