论文部分内容阅读
原发性心肌病的心电图表现为大家所熟知。伴发于进行性假肥大型肌营养不良者,国内较少报道。本文将其重型——进行性肌营养不良症(Progressive Muscular Dystrophy,PMD)21例患者的心电图分析报道于后。材料和诊断依据作者等曾对浙江部份地区的假肥大型进行性肌营养不良症患者共25个家系作了调查,共查出存活患者39例,全部为男性。诊断依据是:1.家族史,按X染色体性连锁隐性遗传方式遗传;2.临床症状,3.血清磷酸肌酸激酶活性高于正常值(Hughes比色法为110—3239U,中位数505U,而正常健康儿童为
ECG manifestations of primary cardiomyopathy are well known. Accompanied by progressive Duchenne muscular dystrophy, less reported in China. This article reports the ECG analysis of 21 patients with progressive muscular dystrophy (PMD). Materials and Diagnosis According to the authors who had a survey of 25 families of duchenne muscular dystrophy in some parts of Zhejiang Province, a total of 39 survivors were found, all male. The diagnosis is based on: 1. family history, according to the X chromosome recessive genetic inheritance; 2. clinical symptoms, 3. serum creatine kinase activity higher than normal (Hughes colorimetric method for the 110-3239U, the median 505U, while normal healthy children