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我院自1981年～1986年共收治4例以慢性肝炎为首发症状的Wilson病,现报道如下。一般资料男女各2例,年龄13～28岁。例1:女,28岁。肝脾肿大,腹水,胸腔积液,四肢震颤,K-F环(+)。肝功能检查:GPT43U,胆红素34μmol/L,白蛋白14g/L,球蛋白33g/L,γ球蛋白48%。铜氧化酶6 U,尿铜27.2μmol/d.治疗无效死亡.例2:男,19岁。10岁时曾发现“慢肝”.肝脾肿大,腹水,K-F环(+)。肝功能检查:GPT12U,胆红素21μmol/L,HBsAg(-),白蛋白24g/L,球蛋白37g/L,γ球蛋白35g%,凝血酶原时间17.7秒.铜氧化酶7 U,尿铜159μmol/d。经治疗后好转。例3:男,13
Our hospital from 1981 to 1986 were treated with 4 cases of chronic hepatitis as the first symptom of Wilson’s disease are reported below. General information 2 cases of male and female, aged 13 to 28 years old. Example 1: Female, 28 years old. Hepatosplenomegaly, ascites, pleural effusion, limb tremor, K-F ring (+). Liver function tests: GPT43U, bilirubin 34μmol / L, albumin 14g / L, globulin 33g / L, gamma globulin 48%. Copper oxidase 6 U, copper copper 27.2μmol / d. Treatment died. Example 2: Male, 19 years old. Found at age 10 “slow liver.” Hepatosplenomegaly, ascites, K-F ring (+). Liver function tests: GPT12U, bilirubin 21μmol / L, HBsAg (-), albumin 24g / L, globulin 37g / L, gamma globulin 35g%, prothrombin time 17.7 seconds. Copper oxidase 7U, Copper 159 μmol / d. After treatment improved. Example 3: Male, 13