先天性小眼球为先天发育异常,包括小角膜,虹膜脉络膜缺损及眼球震颤。此病可为散发性,也可为遗传性;可以单独存在眼病,也可伴有全身异常。白内障常发生于先天性小眼球。文中总结6人10例先天性小眼球合并白内障接受人工晶体植入术的病人。角膜直径9mm 以上视力恢复较满意,8mm 以下的眼球效果差。这些总结表明人工晶体植入术对先天性小眼球是比较安全和成功的。 Congenital small eyeball is congenital anomalies, including small cornea, iris choroid defect and nystagmus. The disease can be sporadic, but also hereditary; may exist alone eye disease, but also may be associated with systemic abnormalities. Cataracts often occur in congenital small eyeball. The paper summarizes 6 cases of 10 patients with congenital small orbital cataract patients undergoing intraocular lens implantation. Corneal diameter more than 9mm more satisfactory visual acuity, ocular effects below 8mm poor. These findings suggest that intraocular lens implantation is relatively safe and successful for congenital small eyeballs.