纤维结构不良为不常见而原因不明的良性病变 ,与成骨细胞分化及成熟缺陷有关。 1937年 Mc Cune等首称骨形成异常 ,次年 Lichtenstein称为纤维结构不良(fibrous dysplasia)。好发于面及颅骨 ,致畸形与功能障碍。本病例 4 7岁男性 ,左耳平均纯音听阈为 6 5d B,气骨导差为 30 d B? Poor fiber structure is not common and unexplained benign lesions, and osteoblast differentiation and maturity defects. In 1937, Mc Cune and other first bone abnormalities, the next Lichtenstein known as fibrous dysplasia (fibrous dysplasia). Occur in the face and skull, deformity and dysfunction. In this case, a 47-year-old male with a mean pure tone hearing threshold of 6 5 days at left ear and a 30-day B of air-bone conduction difference