慢性家族性和后天性脱髓鞘神经病的区别是重要的,因为后者对皮质类固醇、免疫抑制剂或血浆替换治疗可以有效。通常由病史和体检可以区别,但有时家族史不清楚,神经病的时间不确定以及临床体征不能鉴别。此时,电诊断的特征对二者的区别有帮助。 The distinction between chronic familial and acquired demyelinating neuropathies is important because the latter can be effective for corticosteroids, immunosuppressive agents or plasma replacement therapy. Usually by the medical history and physical examination can be distinguished, but sometimes the family history is not clear, neurological time uncertainty and clinical signs can not be identified. At this point, the characteristics of electrical diagnosis of the difference between the two helpful.