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本文报道特发性Q-T间期延长综合征7例。其中5例家族中发现有本征的症状或(和)Q-T间期延长者。所有病例入院前均有2次以上晕厥发作史,发作前几乎均有明显诱因,5例入院前被误诊为癫痫、心肌炎、心肌炎后遗症或心肌病等。发作时心电图示多源性室性早搏、短阵室性心动过速、间或伴有心室扑动颤动,发作间歇期示QT_c期延长,T波变化。发作时用利多卡因、苯妥英钠、心得安或氯化钾合并异丙肾上腺素可终止室性快速性心律失常。间歇期用心得安及(或)苯妥英钠、酰胺咪嗪可预防发作。
This article reports 7 cases of idiopathic Q-T prolongation syndrome. Five of the five families were found to have intrinsic symptoms or (and) prolonged Q-T intervals. All cases before admission were more than 2 times the history of syncope, almost all before the onset of obvious incentives, 5 cases were misdiagnosed as pre-admission epilepsy, myocarditis, myocarditis sequelae or cardiomyopathy. Episode ECG showed multi-source ventricular premature beats, paroxysmal ventricular tachycardia, or accompanied by ventricular flutter fibrillation, intermittent episodes of QT_c period showed prolonged T wave changes. Episodes with lidocaine, phenytoin sodium, propranolol or potassium chloride combined with isoproterenol to terminate ventricular tachyarrhythmia. Intermittent with peace of mind and (or) phenytoin sodium, amidazine can prevent seizures.