论文部分内容阅读
Wegener肉芽肿病是一种以坏死性肉芽肿和泛发性血管炎为特征的疾病,本病于1931年Klinger首次报告,1936年Wegener证实这是上下呼吸道肉芽肿、肾小球肾炎、广泛坏死性血管炎三联征的疾病。本病有全身型及局限型。前者有上呼吸道、肺、肾脏病变,病情重,不治疗可迅速死亡。局限型限于下呼吸道而无肾损害,病情较轻,预后良好。局限型可转变为全身型。国内自1957年以来共报道160余例。我们遇到1例,结合文献复习报道如下。
Wegener’s granulomatosis is a disease characterized by necrotizing granulomatosis and generalized vasculitis, first reported by Klinger in 1931 and confirmed by Wegener in 1936 as upper and lower respiratory granulomas, glomerulonephritis, extensive necrosis Vasculitis triple disease. The disease has systemic and limitations. The former has the upper respiratory tract, lung, kidney disease, illness, without treatment can die quickly. Limitations limited to the lower respiratory tract without renal damage, mild illness, the prognosis is good. Limitations can be transformed into full body type. More than 160 cases have been reported in China since 1957. We encountered 1 case, combined with the literature review reported below.