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作者报告7例原发肾上腺皮质功能不全病例。幼儿期发病,确诊年龄为4～12岁。其中男性2例,女性5例。5名女孩和1名男孩有糖及盐皮质激素衰竭,另1名男孩是单纯糠皮质激素衰竭。 幼儿的Addison氏病同成人一样,也是以糖及盐类皮质激素衰竭力特征的。大多数具有全身不适、体重减轻、皮肤及粘膜色素沉着、厌食、恶心、呕吐、低血糖及低血压等重要临床症状。实验检查提示低血红蛋白、低钠,血钾升高及空腹血糖下降。依靠升高的ACTH及ACTH刺激试验,诊断不难。
The authors report 7 cases of primary adrenal insufficiency. Early onset of the disease, the diagnosis of age 4 to 12 years old. Among them, there were 2 males and 5 females. Five girls and one boy had sugar and mineralocorticoid failure, and the other boy had simple corticosteroid failure. Addison’s disease in young children, like adults, is characterized by the breakdown of sugar and salt corticosteroids. Most of them have important clinical symptoms such as general malaise, weight loss, skin and mucous pigmentation, anorexia, nausea, vomiting, hypoglycemia, and low blood pressure. Experimental examinations showed low hemoglobin, low sodium, elevated serum potassium and fasting blood glucose. With elevated ACTH and ACTH stimulation tests, diagnosis is not difficult.