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本文报告我院自1986年以来共收治经病理证实的Langerhans细胞组织细胞增多症15例,其中嗜酸性肉芽肿9例,经手术治疗均愈;LS病1例,经化疗症状好转,但尿崩症不易控制;HSC病2例,1例经手术及化疗后局部病灶及尿崩症均愈,1例失访;中间型(介于LS病及HSC病之间)3例,用VCR、CTX、强的松化疗后2例愈。另外对该病之病因、发病年龄、临床特征、影像学检查、治疗方法和预后进行较为详细的分析和讨论。
This article reports from our hospital since 1986, a total of 15 pathologically confirmed Langerhans cell histiocytosis in 15 cases, including 9 cases of eosinophilic granuloma after surgery were cured; LS disease in 1 case, the symptoms improved after chemotherapy, but diabetes collapse 2 cases of HSC disease, 1 case of local lesion and diabetes insipidus after operation and chemotherapy were cured, 1 case was lost to follow-up; 3 cases of intermediate type (between LS and HSC disease) were treated with VCR, CTX , 2 cases of prednisone after chemotherapy. In addition to the etiology of the disease, the age of onset, clinical features, imaging examination, treatment and prognosis for more detailed analysis and discussion.