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本文报告我院自１９８６年以来共收治经病理证实的Ｌａｎｇｅｒｈａｎｓ细胞组织细胞增多症１５例，其中嗜酸性肉芽肿９例，经手术治疗均愈；ＬＳ病１例，经化疗症状好转，但尿崩症不易控制；ＨＳＣ病２例，１例经手术及化疗后局部病灶及尿崩症均愈，１例失访；中间型（介于ＬＳ病及ＨＳＣ病之间）３例，用ＶＣＲ、ＣＴＸ、强的松化疗后２例愈。另外对该病之病因、发病年龄、临床特征、影像学检查、治疗方法和预后进行较为详细的分析和讨论。
This article reports from our hospital since 1986, a total of 15 pathologically confirmed Langerhans cell histiocytosis in 15 cases, including 9 cases of eosinophilic granuloma after surgery were cured; LS disease in 1 case, the symptoms improved after chemotherapy, but diabetes collapse 2 cases of HSC disease, 1 case of local lesion and diabetes insipidus after operation and chemotherapy were cured, 1 case was lost to follow-up; 3 cases of intermediate type (between LS and HSC disease) were treated with VCR, CTX , 2 cases of prednisone after chemotherapy. In addition to the etiology of the disease, the age of onset, clinical features, imaging examination, treatment and prognosis for more detailed analysis and discussion.