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席汉氏综合征合并产后尿崩症临床上罕见。我院收治1例,报告如下。王某,女,30岁,农民。于1983年11月在家足月分娩,流血过多。产后无乳、闭经、消瘦、乏力、食欲不振、多饮(5000—7500ml/日)、多尿(5000—6000ml/日)。入院前2月常间断发冷、发烧,伴下腹痛,体温有时高达39℃以上。于1985年3月18日入院。体检:体温37.5℃,脉搏94,血压90/70,慢性病客,消瘦,早衰貌。皮肤干燥,弹性差,双眼眶凹陷,头发眉毛稀疏,腋、阴毛缺如,双乳房萎缩,心音低钝,双肺无异常,肝脾不大,下腹部广泛压痛,无肌紧张及反跳痛,未触及包块,膝腱反射减弱。实验室检查:血红蛋白9.7g,白细胞12,080,中性78%,淋巴20%,单核2%。尿常规正常,尿糖阴性,尿比重1.000(3次)。肝功、蛋白电泳,血脂,二氧化碳结合力、尿素氮,空腹血糖、血钾、钠、氯化物在正常范围。心电图示:心肌劳损。X 线胸片及颅片蝶鞍均正常。~(131)I 吸收试验示甲状腺功能低下,血清T_3、T_4含量测定低于正常。
Xi Han’s syndrome combined with postpartum diabetes insipidus clinically rare. 1 case admitted to our hospital, the report is as follows. Wang, female, 30 years old, farmer. In November 1983 full-term delivery at home, excessive bleeding. Postpartum non-milk, amenorrhea, weight loss, fatigue, loss of appetite, drink more (5000-7500ml / day), polyuria (5000-6000ml / day). Few months before admission, intermittent cold, fever, with abdominal pain, sometimes up to 39 ℃ temperature. March 18, 1985 admission. Physical examination: body temperature 37.5 ℃, pulse 94, blood pressure 90/70, chronic disease, weight loss, premature aging appearance. Dry skin, poor elasticity, orbital depression, hair sparse eyebrows, pubic hair missing, double breast atrophy, low heart sound blunt, no abnormal lungs, liver and spleen is not large, the lower abdomen, extensive tenderness, no muscle tension and rebound tenderness , Did not touch the mass, knee tendon reflex decreased. Laboratory tests: hemoglobin 9.7g, leukocytes 12,080, 78% neutral, lymph 20%, mononuclear 2%. Urine routine, urine negative, urine specific gravity 1.000 (3 times). Liver function, protein electrophoresis, blood lipids, carbon dioxide binding, urea nitrogen, fasting blood glucose, serum potassium, sodium, chloride in the normal range. ECG shows: myocardial strain. X-ray and cranial sella were normal. ~ (131) I absorption test showed hypothyroidism, serum T_3, T_4 content was lower than normal.