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白塞氏综合征(Behcet Syndrome)又称为眼、口、生殖器综合征。本病自1937年Behcet氏报告以来,已被公认为是一个独立的疾病。临床以反复发作的口腔粘膜溃疡、外阴溃疡及眼虹膜睫状体炎三组症状作为诊断的主要依据。近年来,许多报导指出,本病不仅表现在口腔、眼、生殖器的损害,尚可侵犯皮肤、关节、消化道、血管和神经系统,造成多脏器的损害,属于一种全身性炎症性疾患。其次,由于血清免疫学研究进展,对本病有了进一步的认识,并为治疗开辟了新的途径。
Behcet syndrome (Behcet Syndrome), also known as eye, mouth and genital syndrome. The disease has been recognized as an independent disease since Behcet’s report in 1937. Clinical recurrent episodes of oral mucosal ulcers, vulvar ulcers and eye iridocyclitis three symptoms as the main basis for the diagnosis. In recent years, many reports pointed out that the disease not only in the mouth, eyes and genital damage, but also violations of the skin, joints, digestive tract, blood vessels and nervous system, causing multiple organ damage, is a systemic inflammatory disease . Second, due to the progress of serum immunology, we have further knowledge of the disease and opened up new avenues for treatment.