Wegener 氏肉芽肿病在病理上为小动脉纤维素性坏死和肉芽肿损害,临床上为呼吸道、肾、关节、皮肤,眼部等病变综合症。虽屡见报道,但早期表现在眼部者极为少见,国内天津眼科医院于1974年曾报告一例,现将我们遇到一例长期误诊为“蚕蚀 Wegener’s granulomatosis in the pathology of arteriolar fibrosis and granuloma damage, clinically for the respiratory tract, kidney, joint, skin, eye and other lesion syndrome. Although often reported, but the early performance in the eye were extremely rare, the domestic Tianjin Eye Hospital in 1974 had reported a case, now we encounter a case of long-term misdiagnosis as ”