原发肾神经纤维瘤是一种罕见的肾脏良性肿瘤，国内外报道极少，1995年12月，我们手术切除并经病理证实1例，现报告如下：患者，男性，45岁，右中下腹钝痛半月，右侧腹部饱满，经CT、B超示右腹膜后占位，考虑右腹膜后肿瘤。查体：于右侧腹可触及一巨大肿物，上极位于右肋缘以上 Primary renal neurofibroma is a rare renal benign tumor, very few reports at home and abroad, in December 1995, we surgically removed and confirmed by pathology, are reported as follows: Patients, men, 45 years old, right lower quadrant Duchenne half a month, the right abdomen full, by CT, B ultrasound showed right retroperitoneal space, consider the right retroperitoneal tumor. Physical examination: in the right flank can reach a huge tumor, the upper right rib margin above