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永存原始玻璃体增生症 (persistenthyperplasticprimaryvitreous ,PHPV)是一种少见的先天性眼球发育异常 ,临床表现为一系列眼部异常 ,包括白瞳症 ,小眼球 ,前部或 /和后部玻璃体血管残留。继发性青光眼、牵拉性视网膜脱离是视力丧失的常见原因。有手术适应证的病例及时手术对
Persistent hyperplastic primary vitreous disease (PHPV) is a rare congenital ocular dysplasia characterized clinically by a series of ocular abnormalities including pupil disease, small eyeballs, anterior and / or posterior vitreous remnant. Secondary glaucoma, traction retinal detachment is a common cause of vision loss. A case of surgical indications and timely surgery