Pulmonary mucormycosis is an uncommon and often fatal opportunistic fungal infection caused by fungi in the class zygomycetes of the order mucorales. As a rare clinical entity characterized by acute onset, rapid progression and high mortality rate, pulmonary mucormycosis often results in fatal consequences within two years after the onset, and can be easily misdiagnosed.1,2 Here we report a case of pulmonary mucormycosis for which a definite diagnosis had not been established until 6 years after the initial onset.