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特发性间质性肺炎(idiopothic interstitial pneumonias.1iPs)是由一组不同的疾病构成,包括寻常型间质性肺炎(usual interstitial pneumonia,UIP)、非特异性间质性肺炎(nonspecific interstitial pneumonia,NSIP)、呼吸性细支气管炎-间质性肺病(respiratory bronchiolitis—interstitial lung disease,RB—ILD)、急性间质性肺炎(acute interstit