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本文报道17例经钡灌肠、内窥镜、手术探查及病理检查确诊的小儿肠道结节状淋巴样增生症。11例表现为肠套叠,其中7例有反复发作史;其余各例表现为便血、反复腹痛,1例无症状。14例测定免疫球蛋白(Ig),10例异常,7例以Ig增高为主,有1例结核菌素试验强阳性,3例Ig低下。14例都有肠道粘膜及粘膜下重度淋巴细胞浸澜及反应性淋巴滤泡增生,提示该症存在抗原持续刺激和机体免疫调节网络中对淋巴细胞增殖的负反馈机制低下或失控,结合我们的体会对这个并非罕见的小儿疾病提出处理与探讨的建议。
This article reports 17 cases of intestinal nodular lymphoid hyperplasia diagnosed by barium enema, endoscopy, surgical exploration and pathological examination. 11 cases showed intussusception, of which 7 cases had recurrent history; the remaining cases showed blood in the stool, repeated abdominal pain, 1 case asymptomatic. 14 cases of immunoglobulin (Ig) determination, 10 cases of abnormalities, 7 cases of Ig-predominant, 1 case of tuberculin test strongly positive, 3 cases of Ig low. 14 cases have intestinal mucosa and submucosal lymphocytes infiltrating severe and reactive lymphatic follicular hyperplasia, suggesting that the existence of antigen in the disease continued to stimulate and the body’s immune regulatory network of lymphocyte proliferation negative feedback mechanism is low or out of control, combined with our The experience of this is not uncommon pediatric disease proposed treatment and discussion of the proposal.