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目的 :总结 9例先天性长QT综合征 (LQTS)的临床特点及相应的治疗效果。方法 :采集 9例患者的临床病史 ,接受静息和运动心电图、超声心动图及电解质检查 ,随访观察治疗效果。结果 :9例中 ,8例发作与运动或情绪激动有关 ,使用普奈洛尔或普奈洛尔加起搏器治疗 ;1例在睡眠中发病 ,使用临时起搏器加美西律治疗。1例因停药死亡 ,其余随访效果满意。结论 :针对LQTS患者的临床特点采用相应的治疗 ,可取得较满意的疗效
Objective: To summarize the clinical features and corresponding therapeutic effects of nine cases of congenital long QT syndrome (LQTS). Methods: Nine patients with clinical history, resting and exercise ECG, echocardiography and electrolyte examination were followed up to observe the therapeutic effect. RESULTS: Of the 9 patients, 8 had seizures associated with exercise or emotional excitement, were treated with propranolol or propranolol plus a pacemaker, and 1 had onset of sleep using a temporary pacemaker plus mexiletine. One patient died of drug withdrawal, the rest of the follow-up results were satisfactory. Conclusion: The clinical features of patients with LQTS using the appropriate treatment can be more satisfactory results