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报告8例Ebstein畸形,均有心功能减退,主要症状为心悸、砰吸困难和紫绀等。心脏B超和右心X线造影均已确诊。心导管检查结果与心衰程度相一致。按右心血流动力学资料分为右室压力升高期、右室功能代偿期,右室功能失调期3期。心脏B超和声学造影有助于诊断。并对本病患者紫绀的发生,卵圆孔开放的机理以及诊断问题作了讨论。
Eight cases of Ebstein’s deformity were reported, both had hypokalemia. The main symptoms were palpitation, difficulty breathing and cyanosis. B ultrasound and right heart X-ray angiography have been diagnosed. Cardiac catheterization results consistent with the degree of heart failure. According to right hemodynamic data is divided into right ventricular pressure rise, compensatory right ventricular function, right ventricular dysfunction in 3. Heart B-ultrasound and angiography help diagnose. And the incidence of cyanosis in patients with this disease, the mechanism of the opening of the foramen ovale and the diagnosis of the problem were discussed.