胆道闭锁是一种婴儿胆汁淤积性疾病,有大约20%的病例还伴有其他解剖结构的异常。这些常为内脏定位和偏侧异位的缺陷,可导致内脏异位综合征及复合性心脏缺陷综合征。作者描述了1例胆道闭锁伴左心室 Biliary atresia is an infantile cholestatic disease, with approximately 20% of cases associated with other anatomical abnormalities. These often visceral and hemiplegia localization of defects, can lead to visceral syndrome and complex heart syndrome. The authors describe a biliary atresia with left ventricle