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目的探讨伴雷诺现象(RP)系统性红斑狼疮(SLE)的临床特征。方法回顾性分析2003年1月-2008年10月天津市长征医院收治的伴RP的SLE患者临床资料,并与同期收治的91例无RP的SLE患者进行比较。结果伴RP的SLE患者出现脱发、指/趾末端血管炎、甲周红斑、肺脏受累及心电图改变的频率较高,抗U1RNP,ds-DNA及抗Sm抗体阳性率也明显增高,且该组患者SLEDAI评分高于对照组,差异均有统计学意义(P均<0.05),而两组患者肾损害、血液系统损害及其他实验室指标检查结果差异无统计学意义(P均>0.05)。结论伴RP的SLE患者更易发生系统损害和免疫学异常,疾病活动性明显,应予以足够重视,注意患者系统受累情况。
Objective To investigate the clinical features of Rayleigh phenomenon (RP) systemic lupus erythematosus (SLE). Methods The clinical data of SLE patients with RP treated in Changzheng Hospital of Tianjin from January 2003 to October 2008 were retrospectively analyzed and compared with 91 non-RP-treated SLE patients admitted in the same period. Results The frequency of hair loss, apical vasculitis, erythematous ailments, lung involvement and electrocardiogram changes were significantly higher in SLE patients with RP, and the positive rates of anti-U1RNP, ds-DNA and anti-Sm antibody were also significantly increased. The SLEDAI score was higher than that of the control group (all P <0.05). There was no significant difference between the two groups in the results of renal damage, blood system damage and other laboratory tests (all P> 0.05). Conclusions Patients with SLE with RP are more likely to have systemic damage and immunological abnormalities. The disease activity is obvious and should be paid enough attention. Pay attention to the patients’ systemic involvement.