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本文分析了72例患中、重度感觉神经性聋的病儿。发病原因:26%为获得性,分别为新生儿脑膜炎、新生儿窒息、21三染色体、先天梅毒和高胆红素血症所引起;24%为遗传性;50%病因不明。作出诊断的平均年龄为5.3岁,配戴助听器的平均年龄为6.3岁。听力学检查包括用或不用助听器两种条件下检查:扬扬格阈(ST),语言察觉阈(SDT),纯音均值(PTA),语言识别率(WRS)。语言发育水平评价包括:语言发育延迟年龄和语言发育指数,后者即患儿语言发育水平所相当的年龄除以实际年龄。结果:本组ST均值为61dB,SDT均值
This article analyzes 72 cases of children with moderate and severe sensory nerve deafness. Causes of the disease: 26% were acquired due to neonatal meningitis, neonatal asphyxia, trisomy 21, congenital syphilis and hyperbilirubinemia; 24% were hereditary; 50% were unknown. The average age of diagnosis was 5.3 years and the average age of wearing hearing aids was 6.3 years. The audiological examination included two conditions: with or without hearing aid: ST, SDT, PTA, WRS. The evaluation of language development includes the age of speech development and the language development index, which is equivalent to the level of language development in children divided by the actual age. Results: The average ST in this group was 61dB, the mean value of SDT