先天性胃壁肌层缺损临床上比较少见,但死亡率却很惊人,有文献报告死亡率达83％,我院最近收治1例,经积极抢救,得以存活,现报告如下: 病历摘要:患儿,女,生后6天,于1995年5月28日清晨出现啼哭,拒食,上午10时开始腹胀并逐渐加重,下午5时出现呼吸困难急来我院就诊。检查:T37.7℃,P150次/分,R40次/分,皮肤黄染,口唇紫绀,四肢末稍发凉,心率150次/分, Congenital gastric wall muscle defect clinically rare, but the mortality rate is staggering, the literature reported a mortality rate of 83%, our hospital recently admitted in 1 case, after active rescue, to survive, are as follows: Medical records summary: Children Female, 6 days after birth, crying and refusing to eat in the early morning of May 28, 1995, began bloating at 10 am and gradually increased. At 5 pm, she had difficulty breathing and came to our hospital for medical treatment. Check: T37.7 ℃, P150 beats / min, R40 beats / min, skin yellow dye, cyanotic lips, extremities extremes cold, heart rate 150 beats / min,