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特发性肺含铁血黄素沉着症是一种少见的疾病,主要见于小儿时期,以肺内沉着含铁血黄素为其特征,而其他器官此种病变不明显,我科自1973年以来收治三例,现报告如下。 例1 张×× 男,7岁,住院号103713,1973.3.15入院。主诉:面色苍白,四肢无力,反复低热两年余。患儿自1970年上半年起全身无力,面色苍白,逐渐消瘦并有低热盗汗,经多处医院治疗并输血后病情好转,但仍有反复发作,于入院前10天,上述症状加重,伴有气短而来我院门诊以“贫血原因待查”收入院,病后大小便正常,无出血情况。 入院检查,体温37.7°,脉搏120次,血压110/70,呼吸24次,神志清,发育中等,贫血外貌明显,但全
Idiopathic pulmonary hemosiderosis is a rare disease, mainly seen in infancy, characterized by pulmonary hemosiderin, while other organs of this lesion is not obvious, our department has been treated since 1973 Three cases are as follows. Example 1 × × male, 7 years old, hospital number 103713,1973.3.15 admission. Chief complaint: pale, limb weakness, repeated fever more than two years. Since the first half of 1970, children with general weakness, pale, gradually thin and have low fever night sweats, after multiple hospital treatment and blood transfusion improved, but there are still recurrent, 10 days before admission, the above symptoms aggravated, accompanied by Shortness of breath to our hospital outpatient to “anemia to be investigated” income hospital, normal illness and urine, no bleeding. Admission examination, body temperature 37.7 °, pulse 120 times, blood pressure 110/70, breathing 24 times, clear consciousness, developmental medium, anemic appearance, but all