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目的探讨眼眶血管内皮瘤(hemangioendothelioma,HE)及血管外皮瘤(hemangiopericytoma,HPC)的MRI表现,旨在提高其影像学诊断水平。方法回顾性分析10例眼眶HE及HPC的MRI表现,均行MRI平扫及动态增强扫描。结果 10例中8例发生于眶隔后肌锥外间隙,2例发生于眶隔前;9例表现为形态规整的圆形或类圆形,边界清楚,1例可见分叶;平扫8例表现为等T1、长T2信号,7例可见点、条状血管流空信号;动态增强扫描显示肿瘤早期即出现明显强化,9例表现为明显均匀强化,1例强化不均匀,内部可见囊变区。结论眼眶HE及HPC为富血供脉管性肿瘤,具有一定的影像学特征,MRI平扫及动态增强扫描有助于其影像学诊断。
Objective To investigate the MRI findings of hemangioendothelioma (HE) and hemangiopericytoma (HPC) in order to improve their imaging diagnosis. Methods The MRI findings of 10 cases of orbital HE and HPC were retrospectively analyzed. Both MRI scan and dynamic contrast-enhanced scan were performed. Results Of the 10 cases, 8 occurred in the extrapyramidal space of the posterior orbital septum, 2 occurred in the anterior orbital septum, 9 presented as round or oval-shaped circles with clear boundaries and 1 with visible lobes. Cases showed T1, T2 signal, 7 cases visible, strip vascular empty signal; dynamic contrast-enhanced scan showed that the tumor was significantly enhanced, 9 cases showed significantly uniform enhancement, 1 case of uneven enhancement, the internal visible capsule Variable area. Conclusions The orbital HE and HPC are blood-rich vessels for vasculature and have certain imaging features. MRI plain scan and dynamic contrast-enhanced scan are helpful for imaging diagnosis.