脑外血管外皮肉瘤,是一种罕见的软组织恶性肿瘤,术前诊断困难。国内仅偶见报道。 患者男,17岁,因间断性头痛,呕吐20天,视物模糊10天入院。检查:精神不振,反应迟钝。左眼视力减退,双眼底视孔头水肿,渗出。运动感觉正常;右上肢腱反射(+++),双下肢腱反射(+++),巴氏征(+)。MRI示:左额叶前方有5×6cm~2占位性病变,椭圆形,边界清楚,中 Extracranial vascular endothelial sarcoma, is a rare malignant tumor of soft tissue, preoperative diagnosis difficult. Domestic occasional reports. Male patient, 17 years old, due to intermittent headache, vomiting for 20 days, blurred vision 10 days admitted to hospital. Check: sluggish, unresponsive. Left eye vision loss, binocular bottom hole edema, exudation. Exercise feeling normal; right upper extremity tendon reflex (+++), lower extremity tendon reflex (+++), Pakistan’s sign (+). MRI showed: frontal left front 5 × 6cm ~ 2 space-occupying lesions, oval, border clear, medium